A disease‐specific activity index for Wegener's granulomatosis: Modification of the Birmingham Vasculitis Activity Score

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منابع مشابه

Key words: vasculitis, ANCA, granulomatosis with polyangiitis, microscopic polyangiitis, Birmingham Vasculitis Activity Score, Vasculitis Damage Index, cyclophosphamide, rituximab

NIHR Musculoskeletal Biomedical Research Unit, Nuffield Department of Orthopaedics, Rheumatology and Musculoskeletal Science, University of Oxford, Oxford, United Kingdom. Raashid Luqmani, DM, FRCP, Professor Please address correspondence to: Prof. Raashid Luqmani, NIHR Musculoskeletal Biomedical Research Unit, Nuffield Department of Orthopaedics, Rheumatology and Musculoskeletal Science, Unive...

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Assessment of the item selection and weighting in the Birmingham vasculitis activity score for Wegener's granulomatosis.

OBJECTIVE To assess the Birmingham Vasculitis Activity Score for Wegener's Granulomatosis (BVAS/WG) with respect to its selection and weighting of items. METHODS This study used the BVAS/WG data from the Wegener's Granulomatosis Etanercept Trial. The scoring frequencies of the 34 predefined items and any "other" items added by clinicians were calculated. Using linear regression with generaliz...

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A cross-sectional study of the Birmingham Vasculitis Activity Score version 3 in systemic vasculitis.

OBJECTIVE Assessment of disease activity in vasculitis can be achieved using the BVAS, a clinical checklist of relevant symptoms, signs and features of active disease. The aim of this study was to revalidate the BVAS version 3 (BVAS v. 3) in a cohort of patients with systemic vasculitis. METHODS A total of 238 patients with vasculitis from seven countries in Europe were evaluated at a single ...

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Birmingham vasculitis activity score, disease extent index and complement factor C3c reflect disease activity best in hepatitis C virus-associated cryoglobulinemic vasculitis.

OBJECTIVE Clinical measures of vasculitis activity (Birmingham vasculitis activity score = BVAS) and disease extent (Disease Extent Index = DEI), serological and immunological parameters were evaluated for the monitoring of hepatitis C virus (HCV)-associated cryoglobulinemic vasculitis (CV), treated with either cyclophosphamide or interferon-alpha 2b depending on disease severity. METHODS Ser...

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ENT manifestations of Wegeners granulomatosis.

Wegeners granulomatosis is a necrotizing granulomatous vasculitis with multisystemic involvement. We present two cases of Wegener's presenting with otological manifestations as the first symptom. These symptoms are subtle and diagnosis may be easily overlooked. Hence a high index of suspicion is required. Early diagnosis and treatment goes a long way in improving the outcomes and in preventing ...

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ژورنال

عنوان ژورنال: Arthritis & Rheumatism

سال: 2001

ISSN: 0004-3591,1529-0131

DOI: 10.1002/1529-0131(200104)44:4<912::aid-anr148>3.3.co;2-x